What are Autoinflammatory Diseases?

doi:10.5005/jp-journals-10081-1275

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What are Autoinflammatory Diseases?

Citation Information : What are Autoinflammatory Diseases?. Pediatr Inf Dis 2020; 2 (3):122-124.

DOI: 10.5005/jp-journals-10081-1275

License: CC BY-NC 4.0

Published Online: 28-09-2020

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Abstract

Autoinflammatory diseases/syndromes are a new group of heterogeneous diseases characterized by “spontaneous onset of inflammation with no evidence of infection, autoimmunity or allergy and occur due to a defect in the innate immune system.” With the advancement of molecular genetics and next-generation sequencing technologies, new diseases are being added to this list every year. In this review, a brief description of a few autoinflammatory diseases would be provided along with a clinical approach. Salient clinical features have been highlighted.

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