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VOLUME 1 , ISSUE 4 ( October-December, 2019 ) > List of Articles


Fuchs Syndrome: An Uncommon Entity of Stevens–Johnson Syndrome beyond Drugs

Muhammed Hafis, Kaavil V Arun

Keywords : Fuchs syndrome, Mycoplasma, Steven–Johnson syndrome

Citation Information : Hafis M, Arun KV. Fuchs Syndrome: An Uncommon Entity of Stevens–Johnson Syndrome beyond Drugs. Pediatr Inf Dis 2019; 1 (4):171-173.

DOI: 10.5005/jp-journals-10081-1232

License: CC BY-NC 4.0

Published Online: 03-10-2020

Copyright Statement:  Copyright © 2019; The Author(s).


Background: A rare case of atypical Steven–Johnson syndrome secondary to mycoplasma infection. Case description: An eight-year-old boy presented with a history of fever and cough of 7 days with recent-onset redness and purulent discharge of eyes with multiple oral ulcers for the past 3 days. He was febrile, toxic looking with bilateral conjunctival congestion, multiple painful ulcers in the mouth, and severe mucositis. Because of cefpodoxime ingestion before the onset of ulcers and redness of eyes, possibility of Steven–Johnson syndrome considered and history of respiratory infection in the absence of skin involvement, atypical Steven–Johnson syndrome secondary to mycoplasma infection (Fuchs syndrome) kept in mind. mycoplasma serology was sent which was reported as positive. Other routine investigations and chest X-ray were normal. Intervention: He was started on IV pulse methylprednisolone for 7 days. He becomes afebrile after the first dose of methylprednisolone. Eye lubricants and topical anti-inflammatory agents continued. A significant reduction in mucositis observed. Later oral corticosteroid continued and tapered and stopped over 2 weeks. Message: Severe mucositis with the background of respiratory infection, Fuchs syndrome should be considered as a differential.

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